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Table of contents
Список сокращений
Предисловие к клиническим рекомендациям по ведению взрослых пациентов с врожденными пороками сердца
1. Общие вопросы
1.1 Введение
1.2 Принципы доказательной медицины в формировании клинических и организационнометодических рекомендаций
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1.3 Общие рекомендации по организации взаимодействия и преемственности в оказании медицинской помощи взрослым с врожденными пороками сердца
1.4 Эпидемиология
1.5 Рекомендации по организации медицинской помощи
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1.6 Рекомендации для профилактики и диагностики инфекционного эндокардита
1.7 Рекомендации по ведению больных при выполнении некардиохирургических хирургических операций
1.8 Рекомендации по планированию беременности
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1.9 Нарушения ритма у взрослых с врожденными пороками сердца
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1.10 Брадикардии
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1.11 Цианотические врожденные пороки сердца
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1.12 Общие рекомендации по ведению пациентов с цианозом
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1.13 Сердечная недостаточность у взрослых пациентов с врожденными пороками сердца
1.14 Рекомендации по трансплантации сердца и комплекса сердце/легкие
2. Дефект межпредсердной перегородки
2.1 Определение
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2.2 Клиническое течение
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2.3 Рекомендации при оценке состояния неоперированных пациентов
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2.4 Дефекты и ошибки в диагностике
2.5 Общие принципы ведения пациентов
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2.6 Рекомендации по наблюдению после оперативного вмешательства
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3. Дефект межжелудочковой перегородки
3.1 Определение
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3.2 Клиническое течение (неоперированный дефект)
3.3 Клинические проявления и оценка состояния неоперированного пациента
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3.4 Диагностические проблемы и ошибки
3.5 Общие принципы ведения пациентов
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3.6. Ключевые вопросы, касающиеся наблюдения пациента
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4. Дефект предсердно-желудочковой перегородки (атриовентрикулярный канал)
4.1 Определение
4.2 Сопутствующие пороки
4.3 Клинические особенности и инструментальное обследование
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4.4 Общие принципы ведения пациентов
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4.5 Ключевые вопросы обследования и наблюдения в отдаленные сроки
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4.6. Беременность и роды
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4.7 Физическая нагрузка
5. Открытый артериальный проток
5.1 Определение и сочетанные пороки
5.2 Клинические проявления и течение
5.3 Рекомендации по обследованию неоперированного больного
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5.4 Дифференциальная диагностика
5.5 Общие принципы ведения взрослых пациентов с врожденными пороками сердца и открытым артериальным протоком
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5.6. Ключевые вопросы обследования и последующего наблюдения
6. Обструкция выводного тракта левого желудочка: клапанная. Подклапанная и надклапанная в сочетании с поражением восходящей аорты и коарктацией
6.1 Определение
6.2 Сопутствующие пороки
6.3 Течение болезни
6.4 Тактика обследования неоперированных пациентов
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6.5 Проблемы и трудности
6.6 Общие принципы ведения пациентов с обструкцией выводного тракта левого желудочка и наличием сопутствующей кардиальной патологии
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6.7 Рекомендации по обследованию и наблюдению пациентов в отдаленные сроки после операции
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6.8 Изолированный аортальный подклапанный стеноз
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6.9 Надклапанный стеноз аорты
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6.10 Рекомендации по обследованию неоперированных пациентов
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6.11 Принципы ведения пациентов с надклапанной обструкцией выводного тракта левого желудочка
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6.12 Коарктация аорты
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6.13 Клинические особенности и оценка состояния неоперированных пациентов
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6.14 Тактика при коарктации аорты
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7. Обструкция путей оттока из правого желудочка
7.1 Определение
7.2. Сочетанные аномалии
7.3 Стеноз клапана легочной артерии
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7.4 Клиническое течение
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7.5 Рекомендации по оценке неоперированного пациента
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7.6 Проблемы и ошибки
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7.7 Стратегии ведения пациентов со стенозом легочной артерии
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7.8 Рекомендации по клиническому обследованию и послеоперационному ведению
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7.9 Обструкция правого сердца, вызванная надклапанным стенозом, стенозом долевых артерий или периферическими стенозами
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7.10 Клинические особенности и обследование неоперированного пациента
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7.11 Рекомендации по обследованию пациентов с надклапанным стенозом, стенозом долевых и периферических легочных артерий
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7.12. Рекомендации по использованию эндоваскулярных методов лечения долевых и периферических стенозов легочной артерии
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7.13 Обструкция «правого» сердца, вызванная стенозом кондуитов или биологических протезов клапана легочной артерии
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7.14 Рекомендации к повторным вмешательствам у пациентов со стенозом кондуита или биологического протеза в позиции легочной артерии
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7.15 Двухкамерный правый желудочек
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7.16 Трудности и «подводные камни»
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7.17 Принципы ведения пациентов
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7.18 Ключевые вопросы оценки и дальнейшего наблюдения
8. Аномалии коронарных артерий
8.1 Определение и сопутствующие пороки
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8.2 Рекомендации по тактике ведения пациентов с патологией коронарных артерий в сочетании с надклапанным аортальным стенозом
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9.3 Рекомендации по тактике ведения пациентов с патологией коронарных артерий в сочетании с тетрадой Фалло
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8.4 Рекомендации по тактике ведения пациентов с патологией коронарных артерий в сочетании с D-транспозицией магистральных артерий после операции артериального переключения
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8.5 Рекомендации по тактике ведения пациентов с врожденной патологией коронарного русла – аномальным отхождением коронарных артерий
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8.6 Рекомендации по тактике ведения пациентов с аномальным отхождением левой коронарной артерии от ствола легочной артерии
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8.7 Рекомендации по тактике ведения пациентов с коронарно-сердечными фистулами
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9. Легочная гипертензия. Физиология комплекса эйзенменгера
9.1 Определение
9.2. Естественное течение
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9.3 Трудности и «подводные камни»
9.4 Рекомендации по оценке состояния пациентов с легочной гипертензией, связанной с врожденным пороком сердца
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9.5. Общие принципы лечения
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9.6 Ключевые моменты оценки результатов исследований и наблюдения за пациентами
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10. Тетрада Фалло
10.1 Определение и сопутствующие пороки
10.2 Естественное течение
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10.3 Клинические особенности и оценка результатов исследований
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10.4 Рекомендации по клиническому обследованию и послеоперационному ведению пациентов
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10.5 Рекомендации для выполнения зондирования у взрослых с тетрадой Фалло
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10.6 Проблемы после коррекции тетрады Фалло
10.7 Общие принципы ведения пациентов после предшествующих операций
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10.8 Рекомендации по проведению хирургического лечения взрослых с предшествующими паллиативными операциями по поводу тетрады Фалло
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10.9 Ключевые вопросы оценки состояния пациентов
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11. D-транспозиция магистральных артерий
11.1 Определение
11.2 Сопутствующие пороки
11.3 Естественное течение (неоперированные пациенты)
11.4 Рекомендации по обследованию оперированных пациентов
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11.5 Клинические особенности и результаты исследований взрослых пациентов с D-транспозицией магистральных артерий после операции артериального переключения
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11.6 Клинические особенности и результаты исследований у взрослых пациентов с D-транспозицией магистральных артерий после операции Rastelli
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11.7 Рекомендации по выполнению диагностической катетеризации после операции
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11.8 Общие принципы ведения пациентов
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11.9 Рекомендации по выполнению электрофизиологического исследования
11.10 Ключевые вопросы послеоперационного ведения и наблюдения
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12. Корригированная транспозиция магистральных артерий
12.1 Определение
12.2 Сопутствующие пороки
12.3 Клиническое течение
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12.4 Клинические особенности и обследование неоперированных пациентов
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12.5 Рекомендации по наблюдению и оценке результатов исследования пациентов с корригированной транспозицией магистральных артерий
12.6 Основные рекомендации по ведению неоперированных пациентов
12.7 Общие принципы ведения пациентов
12.8 Интервенционные методы лечения
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12.8.2 Хирургическая коррекция
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12.9 Аритмии. Кардиостимулятор. Электрофизиологическое исследование
12.10 Рекомендации для послеоперационного наблюдения
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13. Аномалия эбштейна
13.1 Определение
13.2 Естественное клиническое течение
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13.3 Клинические особенности и их оценка у пациентов с аномалией Эбштейна
13.4 Рекомендации по обследованию пациентов с аномалией Эбштейна
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13.5 Рекомендации для диагностических исследований
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13.6 Ведение пациентов с аномалией Эбштейна
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13.7 Показания к выполнению эндоваскулярных вмешательств у взрослых пациентов с аномалией Эбштейна
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14. Атрезия трехстворчатого клапана. Единственный желудочек
14.1 Определение
14.2 Естественное течение
14.3 Клинические проявления, течение заболевания
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14.4 Рекомендации по хирургической тактике у пациентов с единственным желудочком
14.5 Рекомендации по обследованию и диспансерному наблюдению больных после процедуры Fontan
14.6 Клинические проявления и обследование оперированных пациентов
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14.7 Рекомендации для диагностики и катетеризации полостей сердца после коррекции по Fontan
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14.8 Рекомендации по тактике ведения пациентов после первичной коррекции по Fontan
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14.9 Рекомендации по хирургическому лечению после первичной коррекции по Fontan у взрослых
14.10 Показания для обследования и диспансерного наблюдения
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Список отечественной литературы
Список зарубежной литературы
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